Image and content excerpted from the VisualDx clinical decision support system.
VisualDx images show variation in age, skin color, and disease stage. VisualDx has 4 images of Ainhum.
Full text and additional images for Ainhum are available in the following VisualDx packages:
L94.6 – Ainhum
136.0 – Ainhum
SynopsisAinhum, or dactylolysis spontanea, is characterized by the development of a progressive deepening and constricting band (sulcus) that encircles a digit resulting in spontaneous amputation. The disease occurs most commonly in dark-skinned individuals in Africa, Asia, South and Central America, and the United States. Although very rare in the United States, some authors suggest that it is under-diagnosed and overlooked.
Ainhum occurs in 4 progressive stages, which may take years to fully develop. It begins with the formation of the sulcus, next edema results from the deepening of the sulcus, followed by autoamputation, and then, in the final stage, necrosis completes the amputation. The cause of ainhum is unknown, although many etiologies have been suggested, including impaired blood supply to the little toe.
Ainhum should be distinguished from pseudoainhum, which is congenital or associated with other acquired diseases, including psoriasis, disorders of keratinization, connective tissue diseases, and trauma, among others.