Image and content excerpted from the VisualDx clinical decision support system.
VisualDx images show variation in age, skin color, and disease stage. VisualDx has 40 images of Klippel-Trenaunay Syndrome.
Full text and additional images for Klippel-Trenaunay Syndrome are available in the following VisualDx packages:
See descriptions of all packages available or sign up for a Free 30-Day Trial of the Essentials Package.
Q87.2 – Congenital malformation syndromes predominantly involving limbs
759.89 – Other specified congenital anomalies
Klippel-Trenaunay syndrome is also known as hemangiectatic hypertrophy or angio-osteohypertrophy syndrome. Typically, excessive growth of the soft tissues, venous malformations, and port-wine stains (capillary malformations) are seen early in this disease. Additionally, some individuals with Klippel-Trenaunay syndrome have one limb that is longer and larger than the other limb. The syndrome is most frequently diagnosed in infancy or early childhood.