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Central centrifugal cicatricial alopecia
See also in: Hair and Scalp
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Central centrifugal cicatricial alopecia

See also in: Hair and Scalp
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Contributors: Vivian Wong MD, PhD, Mary Gail Mercurio MD, Susan Burgin MD
Other Resources UpToDate PubMed

Synopsis

Central centrifugal cicatricial alopecia (CCCA), also known as central centrifugal scarring alopecia, is a scarring alopecia predominantly affecting middle-aged women of African descent, with a prevalence of 3%-6% in this demographic. CCCA is rare in men and children. There have been rare familial cases, and therefore children of affected individuals should have careful examination of the scalp.

Its cause is likely multifactorial. The hair-grooming factors that are often attributed to CCCA are cornrow and braiding with and without extensions and weaves with sewn-in or glued-on hair, use of hot combs, and frequent use of hair relaxers. However, there are conflicting reports on the potential associations.

Clinical features include a round alopecic patch of the vertex, with symmetrical centrifugal expansion, demonstrating early disease at the periphery, where scarring may be subtle. It is slowly progressive, culminating in shiny, flesh-colored scarring alopecia. Some residual hairs may be found throughout the involved area.

CCCA was formerly referred to as hot comb alopecia and may also be known as follicular degeneration syndrome, pseudopelade in African Americans, and scarring alopecia in African Americans.

Codes

ICD10CM:
L66.8 – Other cicatricial alopecia

SNOMEDCT:
403333002 – Hot comb alopecia

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Differential Diagnosis & Pitfalls

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Therapy

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References

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Last Reviewed: 01/03/2017
Last Updated: 02/28/2019
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Central centrifugal cicatricial alopecia
See also in: Hair and Scalp
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Central centrifugal cicatricial alopecia : Burning skin sensation, Frontal scalp, Focal scarring alopecia, Pruritus, Short broken hairs
Clinical image of Central centrifugal cicatricial alopecia
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