Patients present with ascites, characterized by a buildup of fluid in the abdomen that can cause weight gain, abdominal pain, or dyspnea.
Chylous ascites in the Western world is most often iatrogenic or due to malignancy, cirrhosis, or congenital lymphatic anomalies. In the developing world, infection is the leading cause of chylous ascites. In pediatrics, congenital anomalies account for the majority of cases of chylous ascites.
For more information, see OMIM.
I89.8 – Other specified noninfective disorders of lymphatic vessels and lymph nodes
52985009 – Chylous Ascites
- Malignancy – lymphoma, carcinoid, Kaposi sarcoma, lymphangiomyomatosis
- Cirrhosis – numerous etiologies, such as chronic viral hepatitis (A, B, C, D), alcohol use disorder, nonalcoholic steatohepatitis, autoimmune hepatitis, primary biliary cirrhosis, primary sclerosing cholangitis, Wilson disease, and hemochromatosis
- Infection – tuberculosis, Mycobacterium avium-intracellulare infection, filariasis
- Pancreatitis (acute, chronic)
- Constrictive pericarditis
- Dilated cardiomyopathy
- Nephrotic syndrome
- Whipple disease
- Celiac sprue
- Abdominal trauma
- Postoperative complication – lymphatic duct injury
- Congenital lymphatic disruption (ie, primary lymphatic hyperplasia, Klippel-Trenaunay syndrome, primary lymphatic hypoplasia)
- Radiation treatment
Last Updated: 01/12/2018