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Congenital megaureter in Adult
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Congenital megaureter in Adult

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Contributors: David Sullo MD
Other Resources UpToDate PubMed


A congenital abnormality characterized by a wide, dilated, and/or tortuous ureter. It may be obstructed, refluxing, obstructed and refluxing, or unobstructed and not refluxing. The primary condition is caused by an ureterovesical junction abnormality; the secondary variation is a complication of abnormal bladder or urethra conditions. Males are affected more often. It occurs more commonly on the left side but can occur bilaterally. Primary megaureter is the second most common cause of neonatal hydronephrosis. The condition is often detected antenatally during maternal ultrasonography. Patients with unobstructed megaureter are typically asymptomatic. Findings of symptomatic patients first occur after infancy and include urinary tract infection, abdominal or flank pain, hematuria, uremia, or other indications of decreased kidney function.

Primary presentation of congenital megaureter in adults and adolescents is uncommon, but has been reported. It is often discovered as an underlying condition during work-up for urinary tract infection or renal stones.


Q62.2 – Congenital megaureter

95576001 – Dilatation of ureter

Differential Diagnosis & Pitfalls

Patients typically present with symptoms consistent with the following, and the congenital abnormality is discovered on imaging.

Best Tests

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Last Updated: 01/03/2017
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Congenital megaureter in Adult
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Congenital megaureter : Abdominal pain, Hematuria, Pelvic pain
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