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Congenital self-healing histiocytosis - Skin
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Congenital self-healing histiocytosis - Skin

Contributors: Mari M. Batta DO, Jeffrey D. Bernhard MD, Craig N. Burkhart MD, Dean Morrell MD, Lowell A. Goldsmith MD, MPH, Nancy Esterly MD
Other Resources UpToDate PubMed

Synopsis

Congenital self-healing histiocytosis (Hashimoto-Pritzker disease) is a rare, benign variant of Langerhans cell histiocytosis. It presents at birth or within the first several weeks of life and usually resolves spontaneously within 3–4 months. The skin lesions consist of generalized papules, vesicles, or nodules. The infants are otherwise well. Typically, there are no systemic symptoms. Because it can be difficult to differentiate the condition from Langerhans cell histiocytosis, a skin biopsy, systemic evaluation, and close follow-up should be performed.

Codes

ICD10CM:
D76.3 – Other histiocytosis syndromes

SNOMEDCT:
404160007 – Congenital self-healing histiocytosis

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Last Updated:08/17/2016
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Congenital self-healing histiocytosis - Skin
Congenital self-healing histiocytosis : Scalp, Scattered few, Smooth papules
Clinical image of Congenital self-healing histiocytosis
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