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Cutis verticis gyrata - Hair and Scalp
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Cutis verticis gyrata - Hair and Scalp

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Contributors: Sandy Chira MD, Mary Gail Mercurio MD, Jeffrey D. Bernhard MD, Lowell A. Goldsmith MD, MPH
Other Resources UpToDate PubMed

Synopsis

Cutis verticis gyrata (CVG) is a scalp disorder characterized by folds and furrows that mimic the gyri of the surface of the brain. Symmetric ridges and grooves are most commonly arranged anteroposteriorly on the vertex and occiput. There are three categories of CVG:  primary essential, primary nonessential, and secondary. 

In essential, or solitary, primary CVG, there are no associated findings. In nonessential primary CVG, patients have neurologic, psychiatric, or ophthalmologic comorbidities (eg, intellectual disability, seizures, schizophrenia, and cataracts). There is a male predominance by a ratio of 6:1 in primary CVG. Most patients develop symptoms after puberty, with 90% presenting before age 30.

In secondary CVG, inflammatory, neoplastic, or systemic conditions lead to a cellular infiltration of the dermis, which gives rise to the corrugated appearance of the scalp. Local inflammatory conditions of the scalp that can give rise to CVG include eczema, psoriasis, and folliculitis. Systemic conditions that are associated with CVG include acromegaly, myxedema, amyloidosis, and syphilis. CVG has been associated with Turner syndrome, Klinefelter syndrome, and fragile X syndrome. Secondary CVG affects both sexes equally and can appear at any age.

Codes

ICD10CM:
Q82.8 – Other specified congenital malformations of skin

SNOMEDCT:
51603000 – Cutis verticis gyrata

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Last Updated: 10/01/2018
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Cutis verticis gyrata - Hair and Scalp
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Cutis verticis gyrata : Vertex scalp
Clinical image of Cutis verticis gyrata
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