ContentsSynopsisCodesLook ForDiagnostic PearlsDifferential Diagnosis & PitfallsBest TestsManagement PearlsTherapyReferencesView all Images (18)
Diffuse neonatal hemangiomatosis - Skin
Other Resources UpToDate PubMed

Diffuse neonatal hemangiomatosis - Skin

Contributors: Craig N. Burkhart MD, Dean Morrell MD, Lowell A. Goldsmith MD, MPH, Nancy Esterly MD
Other Resources UpToDate PubMed

Synopsis

Diffuse Neonatal Hemangiomatosis is characterized by multiple hemangiomatous lesions present at birth or developing rapidly within the first few days of life. In diffuse neonatal hemangiomatosis, multiple cutaneous and visceral hemangiomas can lead to life threatening complications. Potential involved organs include GI tract (leading to GI bleeding), larynx, lungs, CNS, spleen and liver. A-V shunts and hepatic involvement can lead to high-output cardiac failure and death. Mortality is estimated to be over 50%. Cerebral hemorrhage is another cause of death. Infants presenting with multiple disseminated hemangiomas need to be evaluated and managed aggressively.

Codes

ICD10CM:
D18.01 – Hemangioma of skin and subcutaneous tissue

SNOMEDCT:
88120000 – Congenital hemangiomatosis

Look For

Subscription Required

Diagnostic Pearls

Subscription Required

Differential Diagnosis & Pitfalls

Best Tests

Subscription Required

Management Pearls

Subscription Required

Therapy

Subscription Required

References

Subscription Required

Last Updated:05/11/2015
Copyright © 2021 VisualDx®. All rights reserved.
Diffuse neonatal hemangiomatosis - Skin
Diffuse neonatal hemangiomatosis : Failure to thrive, Scattered many, Vascular plaque, Widespread distribution, Friable papules, Red
Clinical image of Diffuse neonatal hemangiomatosis
Multiple red and violaceous papules and nodules on the back, buttocks, and thigh. Note also the unrelated gray patches of congenital dermal melanocytosis on the buttocks.
Copyright © 2021 VisualDx®. All rights reserved.