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Eruptive vellus hair cyst - Skin in Child
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Eruptive vellus hair cyst - Skin in Child

Contributors: Chris G. Adigun MD, David Dasher MD, Jeffrey D. Bernhard MD, Sarah Stein MD, Karen Wiss MD, Sheila Galbraith MD, Craig N. Burkhart MD, Dean Morrell MD, Lynn Garfunkel MD, Nancy Esterly MD
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Synopsis

Eruptive vellus hair cysts (EVHCs) are small cystic papules that occur on the trunk and proximal extremities. They generally occur sporadically but may be inherited in an autosomal dominant fashion. They most commonly arise between ages 5 and 10 years as multiple small, hyperpigmented, flesh-colored or reddish papules on the trunk, primarily on the chest and upper abdomen. Usually at least 5 lesions are present. Skin biopsy is diagnostic and will show cystic structures in the mid-to-upper dermis that characteristically contain numerous vellus hairs.

The etiology of EVHCs is unknown, but they are considered to be a developmental anomaly of body hair follicles, where obstruction of the neck of follicular channel leads to cystic dilation of the follicle followed by subsequent retention of vellus hairs and atrophy of the hair bulbs.

EVHCs characteristically present in childhood and adolescence, although cases have been reported in adulthood and in the elderly. Familial cases present at birth or early infancy, whereas sporadic cases tend to develop in the first or second decades of life. No predilection in any ethnicity or either sex has been established.

EVHCs have been associated with steatocystoma multiplex, trichostasis spinulosa, hypohidrotic ectodermal dysplasia, pachyonychia congenita, Lowe syndrome, and chronic renal failure as well as other neurological disorders.

Codes

ICD10CM:
L73.8 – Other specified follicular disorders

SNOMEDCT:
254685008 – Eruptive vellus hair cysts

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Last Updated:07/10/2019
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Eruptive vellus hair cyst - Skin in Child
Eruptive vellus hair cyst : Abdomen, Superior chest, Smooth papules, Multiple cysts
Clinical image of Eruptive vellus hair cyst
A close-up of several skincolored papules with tiny central puncta.
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