ContentsSynopsisCodesLook ForDiagnostic PearlsDifferential Diagnosis & PitfallsBest TestsManagement PearlsTherapyReferencesView all Images (5)
Fibroelastolytic papulosis
Print
Other Resources UpToDate PubMed

Fibroelastolytic papulosis

Print Images (5)
Contributors: Vijay Balakrishnan, Susan Burgin MD
Other Resources UpToDate PubMed

Synopsis

Fibroelastolytic papulosis (FEP) is a rare, benign disorder of unknown etiology that affects elastic fibers and/or collagen fibers in the dermis.

The term FEP encompasses pseudoxanthoma elasticum-like papillary dermal elastolysis (PXE-PDE) and white fibrous papulosis of the neck (WFPN). These are 2 clinically and histopathologically similar conditions that are believed by some to be variants of the same disease spectrum.

FEP has been reported in both men and women, typically those who are between 40 and 80 years old. It presents as asymptomatic or mildly pruritic whitish-yellow, soft papules that tend to coalesce into cobblestone-patterned plaques, usually on the neck. Sometimes, the papules may be more white, discrete, and firm. More rarely affected areas include the supraclavicular region, upper torso, and the flexural and intertriginous areas.

The pathophysiology of FEP is not fully understood, although it has been hypothesized that intrinsic aging plays a key role in its development. The disorder tends to be slowly progressive with time.

Codes

ICD10CM:
L98.8 – Other specified disorders of the skin and subcutaneous tissue

SNOMEDCT:
402681005 – Disorder due to abnormality of dermal elastin

Look For

Subscription Required

Diagnostic Pearls

Subscription Required

Differential Diagnosis & Pitfalls

Best Tests

Subscription Required

Management Pearls

Subscription Required

Therapy

Subscription Required

References

Subscription Required

Last Reviewed: 06/08/2017
Last Updated: 06/19/2017
Copyright © 2019 VisualDx®. All rights reserved.
Fibroelastolytic papulosis
Print 5 Images
View all Images (5)
(with subscription)
Fibroelastolytic papulosis : Neck, Oval configuration, Round configuration, White color, Yellow color, Smooth papules, Smooth plaques
Copyright © 2019 VisualDx®. All rights reserved.