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Keratosis lichenoides chronica
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Keratosis lichenoides chronica

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Contributors: Jennifer Halford, Susan Burgin MD
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Synopsis

Keratosis lichenoides chronica (KLC), also known as Nekam's disease, is a very rare chronic condition mostly seen in adults. It presents with erythematous or violaceous keratotic papules on the lower extremities that form linear and/or reticulated plaques, and a facial eruption that resembles seborrheic dermatitis. It is usually asymptomatic, but pruritus may be an accompanying symptom. The etiology is unknown. Some think KLC to be a variant of lichen planus.

The disease affects both sexes about equally. A majority of the patients in the literature are of Northern European descent, although patients of other ethnicities have also been reported. The mean time to diagnosis of KLC is 9 years given its rarity and similarities to other keratotic skin diseases. While it is a progressive condition, improvement has been reported with aging or in the summer.

KLC is rarely seen in children, where it presents with differing clinical features than in adults. Possible autosomal recessive inheritance has been proposed in these patients.

Codes

ICD10CM:
L82.1 – Other seborrheic keratosis

SNOMEDCT:
373601005 – Keratosis lichenoides chronica

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Last Reviewed: 06/15/2017
Last Updated: 07/17/2017
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Keratosis lichenoides chronica
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Keratosis lichenoides chronica (Adult) : Face, Linear configuration, Reticular configuration, Trunk, Scaly papules, Violaceous
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