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Klippel-Trenaunay syndrome - Skin in Infant/Neonate
See also in: Anogenital
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Klippel-Trenaunay syndrome - Skin in Infant/Neonate

See also in: Anogenital
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Contributors: Craig N. Burkhart MD, Dean Morrell MD, Lowell A. Goldsmith MD, MPH, Nancy Esterly MD
Other Resources UpToDate PubMed

Synopsis

Klippel-Trenaunay syndrome is also known as hemangiectatic hypertrophy or angio-osteohypertrophy syndrome. Typically, excessive growth of the soft tissues, venous malformations and port wine stains (capillary malformations) are seen early in this disease. Additionally, some individuals with Klippel-Trenaunay syndrome have one limb that is longer and larger than the other limb. The syndrome is most frequently diagnosed in infancy or early childhood.

Codes

ICD10CM:
Q87.2 – Congenital malformation syndromes predominantly involving limbs

SNOMEDCT:
59078009 – Klippel-Trenaunay-Weber syndrome

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Last Updated: 05/13/2015
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Klippel-Trenaunay syndrome - Skin in Infant/Neonate
See also in: Anogenital
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Klippel-Trenaunay syndrome : Asymmetric trunk or extremity, Purple color, Vascular plaque, Limb hypertrophy
Clinical image of Klippel-Trenaunay syndrome
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