ContentsSynopsisCodesDifferential Diagnosis & PitfallsBest TestsReferences
Lutembacher syndrome
Print
Other Resources UpToDate PubMed

Lutembacher syndrome

Print Images (1)
Contributors: Michael W. Winter MD, Ryan Hoefen MD, PhD
Other Resources UpToDate PubMed

Synopsis

A rare combination of a congenital heart defect and ostium secundum atrial septal defect with an acquired stenosis of the mitral valve. Although patients may be asymptomatic, electrocardiography contributes to early detection. Common signs and symptoms include fatigue, exertional dyspnea, heart murmur, and palpitations. Percutaneous transcatheter therapies have had successful outcomes in eligible patients. When severe coexisting conditions are present, such as congestive heart failure and pulmonary hypertension, outcomes may not be favorable.

Codes

ICD10CM:
Q21.1 – Atrial septal defect

SNOMEDCT:
204319006  – Lutembacher Syndrome

Differential Diagnosis & Pitfalls

Best Tests

Subscription Required

References

Subscription Required

Last Updated: 06/02/2017
Copyright © 2018 VisualDx®. All rights reserved.
Lutembacher syndrome
Print 1 Images
Lutembacher syndrome : Fatigue, Exertional dyspnea, Heart murmur, Heart palpitations
Copyright © 2018 VisualDx®. All rights reserved.