Prognosis is poor for severely progressed cases due to impaired breathing, concomitant illness, and complications. Life expectancy may be only 3-5 years following diagnosis.
Without a known cure, management focuses on slowing progression, prevention of complications, supplemental oxygen, and medications and treatment therapies to ease symptoms. Lung transplant may be considered.
J84.10 – Pulmonary fibrosis, unspecified
51615001 – Fibrosis of lung