Trichoepithelioma in Child
Solitary, larger trichoepitheliomas may occur. This is frequently associated with large cylindromas on the scalp (turban tumors). Malignant degeneration does not occur, but early onset of associated basal cell carcinomas may occur in patients with multiple trichoepitheliomas (eg, Rombo syndrome or Bazex-Dupré-Christol syndrome).
D23.30 – Other benign neoplasm of skin of unspecified part of face
274898000 – Trichoepithelioma
- Clinically, trichoepithelioma may appear similar to a number of other adnexal neoplasms, including trichoblastoma, tricholemmomas, and syringomas. Occasionally, lesions may mimic molluscum contagiosum, milia, or sebaceous hyperplasia in the newborn. The clustering of multiple papules within the nasolabial folds of multiple family members is highly suggestive of trichoepitheliomas over other diagnoses.
- Histologically, trichoepithelioma may be difficult to distinguish between basal cell carcinoma and microcystic adnexal carcinoma.
- The angiofibromas of tuberous sclerosis are rarely seen on the upper lip, the most common location for trichoepithelioma lesions.
- Multiple trichilemmomas in Cowden syndrome, which include palmar papules and thyroid and breast malignancies.
- Steatocystoma multiplex presents with larger lesions that are cystic.
- Eruptive vellus hair cysts are bluish in color and are usually found on the trunk.