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Tufted angioma - Skin
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Tufted angioma - Skin

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Contributors: Shilpa S. Sawardekar MD, Craig N. Burkhart MD, Dean Morrell MD, Lowell A. Goldsmith MD, MPH, Nancy Esterly MD
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Synopsis

Tufted angioma, previously known as "angioblastoma of Nakagawa," is a rare vascular tumor. The name describes the histological appearance of "tufted" capillary infiltration of the dermis admixed with dilated lymphatic vessels. It is theorized to have a lymphatic origin.

Tufted angioma typically presents at birth (50% of cases) or within the first year of life as a violaceous plaque or nodule that may be painful. Rarely, it presents during childhood or early adulthood. There may be a slight male predominance.

After an initial period of growth, the tumor stabilizes and usually persists; in some patients it may spontaneously, partially, or completely regress.

Tufted angiomas may be associated with a coagulopathy or with Kasabach-Merritt phenomenon (KMP), a potentially life-threatening condition characterized by an enlarging vascular lesion, profound thrombocytopenia, consumptive coagulopathy, and often a microangiopathic hemolytic anemia.

For more information, see OMIM.

Codes

ICD10CM:
D18.01 – Hemangioma of skin and subcutaneous tissue

SNOMEDCT:
254786000 – Tufted angioma of skin

Look For

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Diagnostic Pearls

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Differential Diagnosis & Pitfalls

Tufted angiomas may be associated with a coagulopathy or with KMP.

Best Tests

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Management Pearls

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Therapy

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References

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Last Updated: 03/29/2017
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Tufted angioma - Skin
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Tufted angioma : Arm, Leg, Smooth nodule, Smooth plaque, Trunk, Tumor, Painful skin lesion
Clinical image of Tufted angioma
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