Aggressive angiomyxoma - Anogenital in
Aggressive angiomyxomas most commonly occur in premenopausal women, although tumors in postmenopausal women and scrotal or perineal tumors in men have been documented. They typically present as an asymptomatic insidiously growing mass. Aggressive angiomyxomas are known to infiltrate local structures, but distant metastasis is rare. Reported local recurrence after surgical resection is 35%-72%.
Aggressive angiomyxomas have been associated with estrogen receptor and progesterone receptor positivity, making them susceptible to hormonal stimulation.
D48.1 – Neoplasm of uncertain behavior of connective and other soft tissue
404085001 – Aggressive angiomyxoma
Differential Diagnosis & Pitfalls