Aggressive angiomyxoma - Anogenital in
Alerts and Notices
Synopsis
Aggressive angiomyxomas most commonly occur in premenopausal women, although tumors in postmenopausal women and scrotal or perineal tumors in men have been documented. They typically present as an asymptomatic insidiously growing mass. Aggressive angiomyxomas are known to infiltrate local structures, but distant metastasis is rare. Reported local recurrence after surgical resection is 35%-72%.
Aggressive angiomyxomas have been associated with estrogen receptor and progesterone receptor positivity, making them susceptible to hormonal stimulation.
Codes
ICD10CM:D48.1 – Neoplasm of uncertain behavior of connective and other soft tissue
SNOMEDCT:
404085001 – Aggressive angiomyxoma
Look For
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Diagnostic Pearls
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Differential Diagnosis & Pitfalls
Based on clinical findings:- Bartholin gland cyst
- Gartner duct cyst
- Vaginal polyp or cyst
- Abscess
- Lipoma
- Hernia
- Pelvic organ prolapse
- Pelvic fibromatosis
- Sarcoma botryoides
- Leiomyoma
- Inguinal or perineal hernia
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Management Pearls
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Therapy
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References
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Last Reviewed:03/05/2023
Last Updated:04/03/2023
Last Updated:04/03/2023