Acroangiodermatitis
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Synopsis
Stewart-Bluefarb syndrome refers to acroangiodermatitis arising in the setting of congenital arteriovenous malformations, typically on the lower extremities. The condition is often diagnosed in teenagers or young adults.
The pathophysiology of acroangiodermatitis remains unclear. Some studies suggest that increased production of vasogenic growth factors, following disruption of normal cutaneous vascular perfusion, may play a role.
Codes
ICD10CM:I78.9 – Disease of capillaries, unspecified
SNOMEDCT:
769036006 – Acroangiodermatitis of skin
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Diagnostic Pearls
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Differential Diagnosis & Pitfalls
- Kaposi sarcoma, AIDS-associated
- Kaposi sarcoma, non-AIDS-associated
- Bacillary angiomatosis
- Reactive angioendotheliomatosis
- Stasis purpura – Pathology shows erythrocyte extravasation without prominent vascular proliferation.
- Capillaritis / pigmented purpuric dermatoses
- Telangiectasia – Pathology shows dilated vessels rather than vascular proliferation.
- Petechiae – Pathology shows extravasated erythrocytes without vascular proliferation; self-limited process.
- Vasculitis – More acute onset and can resolve without treatment.
- Ecchymosis (see traumatic purpura) – Appearance is linked to a history of trauma.
- Lichen planus – Pruritic.
- Atrophie blanche – Painful ulcers healing with stellate white scars.
- Lipodermatosclerosis – Indurated, tender, firm plaques.
- Arterial or venous ulcers
- Angiosarcoma
- Hemangioendothelioma (various types)
- Hemangioma
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Therapy
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References
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Last Reviewed:11/17/2020
Last Updated:11/22/2020
Last Updated:11/22/2020