ContentsSynopsisCodesLook ForDiagnostic PearlsDifferential Diagnosis & PitfallsBest TestsManagement PearlsTherapyReferencesView all Images (12)
Angiokeratoma circumscriptum in Adult
Other Resources UpToDate PubMed

Angiokeratoma circumscriptum in Adult

Contributors: Rajini Murthy MD, Susan Burgin MD
Other Resources UpToDate PubMed

Synopsis

Angiokeratoma circumscriptum is a benign, relatively uncommon form of cutaneous vascular ectasia. It presents as one or more dark red, maroon, or blue-black papule, plaque, or nodule that may have a keratotic or verrucous surface. It is most often found unilaterally on a lower limb.

Angiokeratoma circumscriptum has been associated with Klippel-Trenaunay-Weber syndrome (osteohypertrophy of a limb), Cobb syndrome, port-wine stain, cavernous hemangiomas, and arteriovenous fistulas. The condition is present at birth or develops by early childhood, with lesions often increasing in size during adolescence. Female patients are affected more commonly than male patients.

Codes

ICD10CM:
D23.9 – Other benign neoplasm of skin, unspecified

SNOMEDCT:
21848000 – Angiokeratoma circumscriptum

Look For

Subscription Required

Diagnostic Pearls

Subscription Required

Differential Diagnosis & Pitfalls

Best Tests

Subscription Required

Management Pearls

Subscription Required

Therapy

Subscription Required

References

Subscription Required

Last Reviewed:10/04/2021
Last Updated:10/04/2021
Copyright © 2022 VisualDx®. All rights reserved.
Angiokeratoma circumscriptum in Adult
Angiokeratoma circumscriptum : Ankle, Arm, Lower leg, Present at birth, Scaly plaque, Thigh, Unilateral distribution
Copyright © 2022 VisualDx®. All rights reserved.