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Angiokeratoma circumscriptum in Infant/Neonate
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Angiokeratoma circumscriptum in Infant/Neonate

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Contributors: Susan Burgin MD, Craig N. Burkhart MD, Dean Morrell MD, Nancy Esterly MD
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Synopsis

Angiokeratoma circumscriptum is a benign, relatively uncommon cutaneous vascular disorder. The condition is present at birth or develops by early childhood. It may represent a type of capillary-lymphatic malformation. Rarely, these raised papules have been associated with Klippel-Trenaunay-Weber syndrome (osteohypertrophy of a limb).

Codes

ICD10CM:
D23.9 – Other benign neoplasm of skin, unspecified

SNOMEDCT:
21848000 – Angiokeratoma circumscriptum

Look For

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Diagnostic Pearls

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Differential Diagnosis & Pitfalls

The papules can have a cystic component and may be similar in appearance to lymphangioma circumscriptum.

Best Tests

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Management Pearls

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Therapy

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References

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Last Updated: 06/13/2017
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Angiokeratoma circumscriptum in Infant/Neonate
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Angiokeratoma circumscriptum : Ankle, Arm, Lower leg, Purple color, Feet or toes
Clinical image of Angiokeratoma circumscriptum
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