Bronchopulmonary sequestration (BPS) is a rare congenital abnormality of the lungs consisting of a nonfunctional mass of lung parenchyma that lacks communication with the bronchial tree and, instead, receives its blood supply from the systemic circulation. The vast majority (75%-90%) are intralobar, located within the normal lung and lacking their own visceral pleura, or extralobar, which are typically situated between the lower lobe and diaphragm, encapsulated by their own pleura. In 98% of cases, intralobar BPS is located in the lower lobe. Intralobar sequestrations are typically identified after a patient presents with recurrent pulmonary infections. Extralobar sequestrations are typically identified earlier, often in the prenatal period or during childhood.