Capillaritis in Adult
Alerts and Notices
Synopsis

Several distinct clinical entities have been described:
- Schamberg disease: the most common manifestation of PPD
- Purpura annularis telangiectodes (Majocchi disease)
- Eczematid-like purpura of Doucas and Kapetanakis
- Pigmented purpuric lichenoid dermatosis of Gougerot and Blum
- Lichen aureus
- Linear pigmented purpura
- Granulomatous pigmented purpura
Capillaritis is typically asymptomatic but may be pruritic. It is usually a chronic condition with intermittent exacerbations and remissions. There is no geographic or hereditary population predilection. Men appear to be affected more commonly than women.
Codes
ICD10CM:I78.8 – Other diseases of capillaries
SNOMEDCT:
85461008 – Capillaritis
Look For
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Diagnostic Pearls
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Differential Diagnosis & Pitfalls
- Stasis dermatitis
- Mycosis fungoides – a subtype resembling capillaritis has been reported
- Drug-induced nonpalpable purpura
- Fixed drug reaction
- Lichen planus
- Leukocytoclastic vasculitis
- Scurvy
- Idiopathic thrombocytopenic purpura
- Thrombotic thrombocytopenic purpura
- Petechiae from other causes (thrombocytopenia, disseminated intravascular coagulation, etc)
Best Tests
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Management Pearls
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Therapy
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Drug Reaction Data
Below is a list of drugs with literature evidence indicating an adverse association with this diagnosis. The list is continually updated through ongoing research and new medication approvals. Click on Citations to sort by number of citations or click on Medication to sort the medications alphabetically.Subscription Required
References
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Last Reviewed:12/01/2016
Last Updated:01/05/2020
Last Updated:01/05/2020