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Chordoma
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Chordoma

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Synopsis

Chordoma is a rare malignant bone tumor of the axial skeleton, originating in notochordal embryonic remnants. It most often develops in the skull base, sacrum, and along the spinal axis, typically in adults. It tends to grow continuously and threaten invasion of surrounding bone and tissue.
  • Signs and symptoms of intracranial (skull base) tumor are headache, dysphagia, and intermittent diplopia. It can exhibit cranial nerve findings, such as neck pain and facial numbness.
  • In the sacral region and along the spinal axis, common signs and symptoms include localized and regional pain, numbness, and weakness. Urinary and intestinal functions can be impaired.
Management depends on the location of the chordoma. It is typically treated by surgical resection and radiotherapy. Chordoma at the base of the skull and hard-to-reach spinal chordomas tend to recur at a greater rate and have a poorer prognosis if resection fails to remove the complete tumor. Due to the tendency to recur, vigilance in follow-up care is essential.

Codes

ICD10CM:
C41.9 – Malignant neoplasm of bone and articular cartilage, unspecified

SNOMEDCT:
50007008 – Chordoma

References

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Last Updated: 02/07/2017
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Chordoma
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Chordoma (Sacral Chordoma) : Extremities weakness, Numbness, Paresthesias
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