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Corticobasal syndrome
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Corticobasal syndrome

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Contributors: Jamie Adams MD, Richard L. Barbano MD, PhD
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Synopsis

Corticobasal syndrome, also known as corticobasal ganglionic degeneration, is a rare neurodegenerative disorder characterized by progressive movement and cognitive dysfunction. Symptoms are often asymmetric at onset and include parkinsonism (bradykinesia and rigidity), dystonia, myoclonus, apraxia, aphasia, and/or alien limb syndrome. Patients may also present with cognitive, behavioral, or language changes. Typical age of onset is 45-70, and average duration is 6-8 years.

Early on, this disease may be hard to differentiate from other dementias or parkinsonian disorders. There can be clinical overlap with progressive supranuclear palsy and frontotemporal dementias.

Codes

ICD10CM:
G31.85 – Corticobasal degeneration

SNOMEDCT:
18842008 – Corticobasal degeneration

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Differential Diagnosis & Pitfalls

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Therapy

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References

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Last Reviewed: 07/09/2018
Last Updated: 07/09/2018
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Corticobasal syndrome
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Corticobasal syndrome : Aphasia, Babinski sign, Dystonia, Hyperreflexia, Apraxia, Myoclonus, Depression
Copyright © 2019 VisualDx®. All rights reserved.