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Cystic hygroma in Adult
Other Resources UpToDate PubMed

Cystic hygroma in Adult

Contributors: Craig N. Burkhart MD, Dean Morrell MD, Lowell A. Goldsmith MD, MPH
Other Resources UpToDate PubMed

Synopsis

Cystic hygroma is a benign lymphatic malformation characterized as macrocystic, with collections of large lymphatic cysts lined by endothelium. It may occur anywhere on the body but typically involves the neck (75%) or axillae (20%). Less common sites (5%) are the mediastinum, retroperitoneum, abdominal viscera, groin, bones, and scrotum. There is no sex predilection. The frequency is 1 in 6000 births. Most lesions (65%) are present at birth; otherwise, lesions present by the age of 2 years.

Lesions occur in otherwise healthy infants, but there is an association with Turner, Down, Edwards, and Noonan syndromes. Aside from an associated chromosomal abnormality, airway obstruction is the most critical complication.

Infection (16% risk) may cause more swelling, pain, fever, and erythema. Hemorrhage (13% risk) should be considered with an enlarging, painful lesion in a child with evidence of acute blood loss.

Codes

ICD10CM:
D18.1 – Lymphangioma, any site

SNOMEDCT:
399882002 – Cystic hygroma

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References

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Last Updated:01/30/2022
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Cystic hygroma in Adult
A medical illustration showing key findings of Cystic hygroma : Axilla, Neck, Present at birth, Tumor, Unilateral distribution
Clinical image of Cystic hygroma - imageId=2438755. Click to open in gallery.
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