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Diffuse neonatal hemangiomatosis
Other Resources UpToDate PubMed

Diffuse neonatal hemangiomatosis

Contributors: Craig N. Burkhart MD, Dean Morrell MD, Lowell A. Goldsmith MD, MPH
Other Resources UpToDate PubMed

Synopsis

Diffuse neonatal hemangiomatosis is characterized by multiple hemangiomatous lesions present at birth or that develop rapidly within the first few days of life. In diffuse neonatal hemangiomatosis, multiple cutaneous and visceral hemangiomas can lead to life-threatening complications. Potential involved organs include the gastrointestinal (GI) tract (leading to GI bleeding), larynx, lungs, central nervous system, spleen, and liver. Arteriovenous (AV) shunts and hepatic involvement can lead to high-output cardiac failure and death. Mortality is estimated to be over 50%. Cerebral hemorrhage is another cause of death. Infants presenting with multiple disseminated hemangiomas need to be evaluated and managed aggressively.

Codes

ICD10CM:
D18.01 – Hemangioma of skin and subcutaneous tissue

SNOMEDCT:
254782003 – Multiple progressive hemangiomata

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Last Updated:02/01/2022
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Diffuse neonatal hemangiomatosis
Diffuse neonatal hemangiomatosis : Failure to thrive, Scattered many, Vascular plaque, Widespread distribution, Friable papules, Red
Clinical image of Diffuse neonatal hemangiomatosis
Multiple red and violaceous papules and nodules on the back, buttocks, and thigh. Note also the unrelated gray patches of congenital dermal melanocytosis on the buttocks.
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