Potentially life-threatening emergency
Duodenal atresia
Alerts and Notices
Synopsis

Duodenal atresia develops in utero during the first trimester but is not always diagnosed on prenatal screening. Newborns will present with abdominal distension, feeding intolerance, bilious emesis, lethargy, and dehydration.
Codes
ICD10CM:Q41.0 – Congenital absence, atresia and stenosis of duodenum
SNOMEDCT:
51118003 – Congenital atresia of duodenum
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Diagnostic Pearls
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Differential Diagnosis & Pitfalls
- Malrotation with volvulus
- Hirschsprung disease
- Meconium ileus
- Jejunal, ileal, or colonic atresia
- Gastroenteritis
- Tracheal-esophageal fistula
- Intestinal perforation
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Management Pearls
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Therapy
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References
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Last Reviewed:07/02/2018
Last Updated:07/12/2018
Last Updated:07/12/2018