Elephantiasis nostras verrucosa
Causes of nonfilarial chronic lymphedema include conditions that block lymphatic drainage: congestive heart failure, deep vein thrombosis, morbid obesity, recurrent staphylococcal or streptococcal infections, malignancies (such as lymphoma), and prior surgery or trauma.
ENV is a progressive condition that, left untreated, results in ongoing deformity and disability. Complications include lymphorrhea, infection, secondary ulceration, and poor wound healing.
I89.0 – Lymphedema, not elsewhere classified
61624008 – Elephantiasis nostras
Differential Diagnosis & Pitfalls
- Venous stasis dermatitis
- Pretibial myxedema – Bilateral nodules or plaques are present on the pretibial area bilaterally.
- Lymphatic filariasis – Lymphedema is present in lower limbs and possibly genitals and is accompanied by history of foreign travel. It is secondary to infection with filarial worms (filariasis), Wucheria bancrofti, Brugia malayi, and Brugia timori, all of which are transmitted by a mosquito bite.
- Lymphangioma circumscriptum
- Acquired lymphangiectasia
- Tuberculous lymphangitis (see tuberculosis)
- Deep venous thrombosis
- Kaposi sarcoma
- Stewart-Treves syndrome