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Eosinophilic pustular folliculitis in infancy in All Ages
Other Resources UpToDate PubMed

Eosinophilic pustular folliculitis in infancy in All Ages

Other Resources UpToDate PubMed

Synopsis

A rare self-limited disorder of unknown cause characterized by multiple pustules on a red base with crusting on the scalp and brow. Sometimes the face, neck, trunk, and extremities are involved. Pustules are sterile. Patients may have associated leukocytosis and eosinophilia. Some question whether it is merely an infantile variant of adult eosinophilic pustular folliculitis (Ofuji disease), but the course and clinical presentation differs. About 40 cases have been reported. All cases reported began in infants younger than 1 year, but lesions occurred for 3 months to 5 years before resolving.

Codes

ICD10CM:
L73.8 – Other specified follicular disorders

SNOMEDCT:
403845000 – Neonatal eosinophilic pustular folliculitis

References

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Last Updated:11/03/2015
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Eosinophilic pustular folliculitis in infancy in All Ages
A medical illustration showing key findings of Eosinophilic pustular folliculitis in infancy : Crust, Erythema, Eyebrow, Folliculitis, Pustule, Scalp, Trunk, Cheeks
Clinical image of Eosinophilic pustular folliculitis in infancy - imageId=1836643. Click to open in gallery.  caption: 'Numerous tiny papules and crusts on the forehead.'
Numerous tiny papules and crusts on the forehead.
Copyright © 2026 VisualDx®. All rights reserved.