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Erythromelanosis follicularis faciei et colli
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Erythromelanosis follicularis faciei et colli

Contributors: Molly Weinberg MD, Susan Burgin MD
Other Resources UpToDate PubMed

Synopsis

Erythromelanosis follicularis faciei et colli (EFFC) is a rare dermatosis that presents with well-demarcated erythematous facial patches, hyperpigmentation, and follicular papules on the face and neck. There is often associated alopecia of the vellus hairs within the affected area. There is no atrophy or scarring.

The most common locations are the cheeks, preauricular area, and submandibular regions; however, the eyebrows, chin, and pinnae may also be involved. EFFC is typically bilateral. Onset is usually in the second decade, and males are reported to be affected more frequently than females. Most cases are described in people of Asian descent; however, there are many reports in people of Northern European descent as well.

EFFC is typically asymptomatic; however, pruritus or burning may accompany the cutaneous findings. Photosensitivity has been reported.

The etiology of EFFC is unknown. Genetic predisposition, abnormal autonomic nervous system functioning, and sun exposure have been postulated to contribute to its pathogenesis.

There is a well-established association of EFFC with keratosis pilaris (KP), and some authors have suggested that EFFC may be a variation of KP atrophicans.

Codes

ICD10CM:
L53.8 – Other specified erythematous conditions

SNOMEDCT:
78631004 – Erythromelanosis follicularis of face AND/OR neck

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Last Reviewed:02/12/2020
Last Updated:02/23/2020
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Erythromelanosis follicularis faciei et colli
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Erythromelanosis follicularis faciei et colli
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