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Fibrous hamartoma of infancy in Child
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Fibrous hamartoma of infancy in Child

Contributors: Gabriela Ocasio Diaz BA, Andrea C. Medina González MD, Susan Burgin MD
Other Resources UpToDate PubMed

Synopsis

Fibrous hamartoma of infancy is a rare, benign, hamartomatous soft tissue tumor that appears within the first 2 years of life. It presents as a painless solitary nodule, tumor, or plaque that is commonly located on the trunk or arms, especially in the axillary, shoulder, or pubic region. Male infants are affected more frequently than female infants.

Fibrous hamartoma may be congenital, and most reported cases were noted in the first year of life. Slow growth up to the age of 5 years is typical, and a few cases have shown spontaneous regression. Rarely, multiple lesions are present.

In a recent study of 145 cases, 2 cases were found to have sarcomatous features histopathologically. The clinical significance of this phenomenon is not yet clear.

Codes

ICD10CM:
D21.9 – Benign neoplasm of connective and other soft tissue, unspecified

SNOMEDCT:
56364004 – Fibrous hamartoma of infancy

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Last Reviewed:01/27/2021
Last Updated:01/27/2021
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Fibrous hamartoma of infancy in Child
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Fibrous hamartoma of infancy : Arm, Axilla, Shoulder, Smooth nodule, Trunk, Inguinal region, Genital
Clinical image of Fibrous hamartoma of infancy
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