Infantile perianal pyramidal protrusion
See also in: AnogenitalAlerts and Notices
Synopsis

Three subtypes are distinguished:
- Constitutional
- Related to constipation
- Related to lichen sclerosus
Affected children often have a history of constipation, which may in turn may be a presenting symptom of lichen sclerosus. Other associations include local irritation secondary to wiping.
Codes
ICD10CM:Q82.9 – Congenital malformation of skin, unspecified
SNOMEDCT:
199879009 – Congenital anomaly of skin
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Differential Diagnosis & Pitfalls
- Trauma
- Condyloma acuminatum
- Hemorrhoid
- Granulomatous lesion of inflammatory bowel disease (eg, Crohn disease, ulcerative colitis)
- Rectal prolapse
- Sexual abuse
- Perianal pseudoverrucous papules and nodules
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Last Reviewed:03/17/2020
Last Updated:03/18/2020
Last Updated:03/18/2020
Infantile perianal pyramidal protrusion
See also in: Anogenital