Inherited patterned lentiginosis (IPL) is an extremely rare, autosomal dominant condition reported in patients of African descent, especially those with mixed American Indian heritage. It is characterized by lentigines occurring primarily on the face, including the lips; they may also be found on the buttocks, elbows, hands, and feet. They initially appear during infancy or childhood and increase in number with age. There is no predilection for sun-exposed skin, and the color of macules does not vary with change in season. The mucous membranes are typically not affected.