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Keratosis follicularis squamosa
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Keratosis follicularis squamosa

Contributors: Molly Weinberg MD, Susan Burgin MD
Other Resources UpToDate PubMed

Synopsis

Keratosis follicularis squamosa (Dohi) (KFS) is a follicular keratinizing disorder that has predominantly been reported in Japan. Individuals are most commonly in their third and fourth decade, and there is a slight female predominance.

In KFS, asymptomatic, flat, scaly papules with slightly raised borders and central follicular prominence develop on the lower trunk and thighs. The cause is unclear. Familial occurrence has been described in a small number of cases, and a locus on chromosome 7p14.3-7p12.1 was identified in one large kindred. In some cases, positive staphylococcal cultures have been obtained from the affected follicles; other cases have been linked to friction. A single case was associated with pseudoacanthosis nigricans.

Codes

ICD10CM:
L11.0 – Acquired keratosis follicularis

SNOMEDCT:
238641006 – Acquired keratosis follicularis

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Last Reviewed:02/26/2020
Last Updated:02/26/2020
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Keratosis follicularis squamosa
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Keratosis follicularis squamosa
Copyright © 2021 VisualDx®. All rights reserved.