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Klippel-Trenaunay syndrome in Child
See also in: Anogenital
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Klippel-Trenaunay syndrome in Child

See also in: Anogenital
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Contributors: Craig N. Burkhart MD, Dean Morrell MD, Lowell A. Goldsmith MD, MPH
Other Resources UpToDate PubMed

Synopsis

Klippel-Trenaunay syndrome is also known as hemangiectatic hypertrophy or angio-osteohypertrophy syndrome. Typically, excessive growth of the soft tissues, venous malformations, and port-wine stains (capillary malformations) are seen early in this disease. Additionally, some individuals with Klippel-Trenaunay syndrome have one limb that is longer and larger than the other limb. The syndrome is most frequently diagnosed in infancy or early childhood.

For more information, see OMIM.

Codes

ICD10CM:
Q87.2 – Congenital malformation syndromes predominantly involving limbs

SNOMEDCT:
721105004 – Klippel Trenaunay syndrome

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Last Updated: 02/25/2019
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Klippel-Trenaunay syndrome in Child
See also in: Anogenital
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Klippel-Trenaunay syndrome : Asymmetric trunk or extremity, Purple color, Vascular plaque, Limb hypertrophy
Clinical image of Klippel-Trenaunay syndrome
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