This is considered an otologic emergency due to the possibility of permanent sensorineural hearing loss in the affected ear with or without repair.
Infection, prior ear surgery, and trauma are common causes of fistula formation. In congenital cases, recurrent meningitis may result from the congenital anomaly.
Labyrinthine fistulae are surgically repaired, although rarely they may spontaneously heal. Patients should be instructed to remain on bed rest with an elevated head of the bed.
H83.19 – Labyrinthine fistula, unspecified ear
89097000 – Labyrinthine Fistula
Differential Diagnosis & Pitfalls