Linear atrophoderma of Moulin (LAM) is an atrophic dermal condition characterized by hyperpigmented, unilateral patches or plaques that resemble atrophoderma of Pasini and Pierini (APP) but that follow Blaschko lines on the trunk or limbs. Onset is often sporadic, mostly occurring during childhood or adolescence. While the exact etiology of LAM is unknown, it may reflect a combination of somatic mosaicism and autoimmunity. No distinguishing risk factors or exposure histories are known.
LAM tends to exhibit a stable, nonprogressive course and typically appears suddenly without preceding inflammation or symptoms.
Linear atrophoderma of Moulin
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Synopsis
Codes
ICD10CM:
L90.8 – Other atrophic disorders of skin
SNOMEDCT:
403395007 – Linear atrophoderma of Moulin
L90.8 – Other atrophic disorders of skin
SNOMEDCT:
403395007 – Linear atrophoderma of Moulin
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Differential Diagnosis & Pitfalls
- APP – Well-circumscribed, depressed patches or plaques with characteristic "cliff-drop" edges that do not follow lines of Blaschko.
- Linear morphea – Often associated with preceding lesion inflammation, induration, and dermal sclerosis on histopathology.
- Linear and whorled hypermelanosis
- Incontinentia pigmenti, stage 3 (hyperpigmented stage)
- Lichen striatus
- Linear epidermal nevus
- Inflammatory linear verrucous epidermal nevus (ILVEN)
- Focal dermal hypoplasia (Goltz syndrome) – Characterized by absent dermal collagen with accompanying dermal adipose tissue on histopathology in newborns or young children.
- Linear porokeratosis – Can present anywhere on the body. While they tend to follow lines of Blaschko, lesions tend to have raised hyperkeratotic, peripheral ridges with accompanying anhidrosis and/or pruritus.
- Pigmented post-herpes zoster scars
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Last Reviewed:07/26/2021
Last Updated:07/26/2021
Last Updated:07/26/2021
Linear atrophoderma of Moulin