Macular lymphocytic arteritis
In a review of 32 cases of MLA, the mean age of onset was 40 years, with onset ranging from 6-73 years. Women and children represented 84% and 6% of all cases that were reviewed, respectively. Individuals of African descent represented the largest ethnic group affected by MLA.
The etiology of MLA is unknown. Overlap of some histological features between MLA and certain stages of cutaneous polyarteritis nodosa (C-PAN) have raised the question of whether MLA actually exists as part of a spectrum with C-PAN.
L95.8 – Other vasculitis limited to the skin
46286007 – Lymphocytic vasculitis of skin
Differential Diagnosis & Pitfalls
- – Most commonly affects sun-exposed areas including the face and neck.
- – Typically presents as gray-blue macules and patches affecting the trunk and proximal extremities.