Malignant peripheral nerve sheath tumor
Neurofibromas may transform into MPNSTs. This is of specific concern in patients with neurofibromatosis, who may have a high number of peripheral nerve tumors.
MPNSTs have a poor prognosis generally, with a worse prognosis in people with large tumors or neurofibromatosis. The primary treatment is surgical resection.
C47.9 – Malignant neoplasm of peripheral nerves and autonomic nervous system, unspecified
404037002 – Malignant peripheral nerve sheath tumor
Differential Diagnosis & Pitfalls