Maturity-onset diabetes of the young
MODY typically presents before age 25. The mutations that cause MODY are most often inherited in an autosomal dominant fashion and all result in some level of impaired effectiveness of the beta cells in the pancreas. These patients do not fit the classic characteristics of either type 1 diabetes mellitus (T1DM; ie, autoantibodies present) or type 2 diabetes mellitus (T2DM; ie, obese, older age). When correctly treated, MODY has a slower progression with less severe outcomes than either T1DM or T2DM.
E13.9 – Other specified diabetes mellitus without complications
609561005 – Maturity-onset diabetes of the young
Differential Diagnosis & Pitfalls