Parry-Romberg syndrome in Child
Alerts and Notices
Synopsis

The tongue and salivary glands may be affected. Associated neurologic and ophthalmic involvement may include migraine headaches, seizures, trigeminal neuralgia, enophthalmos, and eyelid dysfunction.
PRS typically develops in the first or second decade and is more common in females. It occurs spontaneously with no known preceding exposures or genetic predisposition, and is believed to be mediated by autoimmune factors. This syndrome may have an insidious onset and is slowly progressive, ultimately stabilizing after 2-20 years.
Codes
ICD10CM:G51.8 – Other disorders of facial nerve
SNOMEDCT:
718224004 – Progressive hemifacial atrophy
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Diagnostic Pearls
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Differential Diagnosis & Pitfalls
- Bell palsy – Acute facial paralysis leading to facial asymmetry.
- Linear morphea without PRS – Firm, indurated plaques with pigmentary change, with prominent dermal sclerosis on pathology.
- Localized lipodystrophy – Atrophy of subcutaneous fat only.
- Panniculitis
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Management Pearls
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Therapy
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References
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Last Reviewed:07/20/2021
Last Updated:07/20/2021
Last Updated:07/20/2021