Pili annulati - Hair and Scalp
Alerts and Notices
Synopsis

Pili annulati may be acquired but is most commonly inherited in an autosomal dominant pattern. The age of onset is usually 2 years. It is a lifelong condition.
Codes
ICD10CM:Q84.1 – Congenital morphological disturbances of hair, not elsewhere classified
SNOMEDCT:
21926007 – Pili annulati
Look For
Subscription Required
Diagnostic Pearls
Subscription Required
Differential Diagnosis & Pitfalls
- Pseudopili annulati – Likely a variant of pili annulati. Patients present with banding on their hairs due to optical effects from twisted hair. On light microscopy, there are no air-filled bands.
- Monilethrix
- Pili torti
- Bubble hair
Best Tests
Subscription Required
Management Pearls
Subscription Required
Therapy
Subscription Required
References
Subscription Required
Last Reviewed:11/03/2020
Last Updated:01/20/2022
Last Updated:01/20/2022