Poikiloderma vasculare atrophicans (PVA) is considered by some authors to be a rare variant of early patch-stage mycosis fungoides (MF) and by others to be a precursor to MF. It has also been referred to as poikiloderma atrophicans vasculare or poikiloderma vasculare atrophicans of Jacobi-Lane, or "poikilodermatous" variant of MF.

PVA is characterized by atrophic patches with telangiectasia and mottled pigmentation, usually on the trunk and flexural areas. The condition is typically asymptomatic; however, there may be pruritus.

Onset is typically between 40 and 60 years of age, with a slight male predilection. Initial presentation may be with one to a few patches that persist for many years. Over time, the lesions may remain stable in size or gradually enlarge or thicken as well as increase in number. Wrinkled, thin plaques that are not poikilodermatous and that resemble patch-stage MF may also be present.

Progression to a more advanced stage of MF is not reliably predictable, and the disease may remain quiescent for many years or indefinitely.