Primary cutaneous amyloidosis of the auricular concha is an uncommonly encountered form of primary cutaneous amyloidosis (a category which also includes lichen, macular, and nodular amyloidosis and the exceedingly rare entities of poikiloderma-like cutaneous amyloidosis and amyloidosis cutis dyschromica). It is characterized by grouped papules in the concha of one or both ears. The papules are often asymptomatic but may also be pruritic. The term primary cutaneous amyloidosis of the auricular concha was first introduced in the literature in 1988, but it may be the same condition as what was previously called collagenous papules of the auricular conchae.

Primary cutaneous amyloidosis of the auricular concha is generally not associated with underlying systemic amyloidosis or other systemic disease; however, auricular lesions can be seen in the setting of other forms of amyloidosis including systemic amyloidosis. There have been reports of this entity occurring in patients on hemodialysis.