Primary lateral sclerosis
Alerts and Notices
Synopsis

Codes
ICD10CM:G12.29 – Other motor neuron disease
SNOMEDCT:
81211007 – Primary lateral sclerosis
Look For
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Diagnostic Pearls
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Differential Diagnosis & Pitfalls
- Amyotrophic lateral sclerosis
- Spinal muscular atrophy
- Hereditary spastic paraplegia
- Cervical myelopathy
- Transverse myelitis
- Syringomyelia
- Syringobulbia
- Human T-cell leukemia virus type 1 (HTLV-1)-associated myelopathy / tropical spastic paraparesis
Best Tests
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Management Pearls
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Therapy
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References
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Last Reviewed:02/07/2019
Last Updated:01/20/2022
Last Updated:01/20/2022