Pulmonary amyloidosis
Alerts and Notices
Synopsis

Signs and symptoms include cough, dyspnea, wheezing, hemoptysis, increased respiratory rate, pleural effusions, and multiple pulmonary nodules or masses. Pulmonary interstitial amyloidosis is symptomatic if amyloid deposits affect gas exchange. Tracheobronchial amyloidosis can cause airway stenosis, and local parenchymal involvement can present as nodular amyloidosis.
Codes
ICD10CM:E85.9 – Other amyloidosis
SNOMEDCT:
196135008 – Pulmonary amyloidosis
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Diagnostic Pearls
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Differential Diagnosis & Pitfalls
- Lung neoplasm – adenocarcinoma, small cell lung cancer
- Pulmonary sarcoidosis
- Infectious – fungal granulomas, tuberculosis
- Asthma
- Chronic obstructive pulmonary disease (COPD)
- Interstitial lung disease
- Pneumonia (viral, bacterial)
- Pulmonary hypertension
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Therapy
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References
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Last Reviewed:03/27/2019
Last Updated:03/27/2019
Last Updated:03/27/2019