Pulmonary arterial hypertension (PAH)
- Group 1 – Elevation of pressure in the pulmonary arteries (idiopathic, hereditary, toxin induced). Examples include idiopathic PAH, hereditary PAH, and PAH due to connective tissue disease, human immunodeficiency virus (HIV) infection, portal hypertension, congenital heart disease, schistosomiasis, or drug use.
- Group 2 – Elevation of pressure in the pulmonary venous system due to left heart disease.
- Group 3 – Elevation of pressure in the pulmonary venous system due to lung disease or hypoxia.
- Group 4 – Chronic thromboembolic pulmonary hypertension.
- Group 5 – Pulmonary hypertension with unclear or multifactorial mechanisms.
Related topic: Portopulmonary hypertension
I27.0 – Primary pulmonary hypertension
70995007 – Pulmonary Hypertension
- Interstitial lung disease
- Obstructive sleep apnea
- Chronic obstructive pulmonary disease
- Congestive heart failure
- Anemia (see iron deficiency anemia)
- Drug toxicity (chemotherapeutics such as cyclophosphamide and bleomycin; amiodarone, fenfluramine / phentermine, aminorex, toxic rapeseed oil, cocaine, amphetamines)
- Radiation-induced lung disease
- Mitral stenosis
- Scleroderma (see also CREST syndrome)
Last Updated: 03/13/2019