Usually occurs secondary to other congenital abnormalities, congenital diaphragmatic hernia being the most common cause. Other causes include pleural effusions, bladder outlet obstruction, and oligohydramnios, among others. Treatment is supportive and is dependent on the size of fetal lungs and cause of pulmonary hypoplasia. Prognosis is defined by the degree of pulmonary hypertension, extent of hypoplasia, and severity of underlying abnormalities. Survivors may experience long-term lung complications.
Q33.6 – Congenital hypoplasia and dysplasia of lung
80825009 – Congenital hypoplasia of lung
Differential Diagnosis & Pitfalls