Pulmonary veno-occlusive disease
Alerts and Notices
Synopsis
Common findings include exertional dyspnea, lethargy, chest pain, pleural effusion, syncope, orthopnea, and nail clubbing. PVOD may be misdiagnosed as pulmonary hypertension.
There is no current effective treatment, and survival prognosis ranges from a few weeks to a few years.
Codes
ICD10CM:I27.9 – Pulmonary heart disease, unspecified
SNOMEDCT:
89420002 – Pulmonary veno-occlusive disease
Look For
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Diagnostic Pearls
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Differential Diagnosis & Pitfalls
- Pulmonary edema – Echocardiogram will show cardiac enlargement and right ventricular hypertrophy without evidence of pulmonary arterial hypertension.
- Chronic pulmonary thromboembolic disease
- Heart failure
- Mitral stenosis
- Fibrosing mediastinitis
- Sarcoidosis
- Interstitial lung disease
- Pneumoconioses (see pneumoconiosis)
- Pulmonary capillary hemangiomatosis
- Atrial myxoma
- Pulmonary arterial hypertension
Best Tests
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Management Pearls
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Therapy
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Drug Reaction Data
Below is a list of drugs with literature evidence indicating an adverse association with this diagnosis. The list is continually updated through ongoing research and new medication approvals. Click on Citations to sort by number of citations or click on Medication to sort the medications alphabetically.Subscription Required
References
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Last Reviewed:05/07/2019
Last Updated:01/23/2022
Last Updated:01/23/2022