ContentsSynopsisCodesBest TestsReferences
Rhabdoid tumor
Other Resources UpToDate PubMed

Rhabdoid tumor

Other Resources UpToDate PubMed

Synopsis

Very aggressive and malignant embryoma typically found in children and associated with high morbidity. Typically diagnosed after the first year of life; rarely found in adults. Arises in the kidneys or in extrarenal soft tissue. May involve the central nervous system, where it is referred to as atypical teratoid rhabdoid tumor. The condition is associated with chromosomal abnormalities that affect normal tumor suppression. Can metastasize.

Signs and symptoms include abdominal mass, neck mass, fever, irritability, peripheral nerve palsy, respiratory difficulties, and hypertension. Findings may be a result of tumor size and location.

Treatment includes tumor resection, aggressive chemotherapy, and radiotherapy if possible.

Codes

ICD10CM:
C80.1 – Malignant (primary) neoplasm, unspecified

SNOMEDCT:
83118000 – Malignant rhabdoid tumor

Best Tests

Subscription Required

References

Subscription Required

Last Updated:02/23/2016
Copyright © 2021 VisualDx®. All rights reserved.
Rhabdoid tumor
Print  
Rhabdoid tumor : Fever, Abdominal mass, Hematuria, Irritability, BP increased
Copyright © 2021 VisualDx®. All rights reserved.